Pablo Ranea Robles

Pablo Ranea Robles

Postdoc


Publication year:
  1. A mitochondrial long-chain fatty acid oxidation defect leads to transfer RNA uncharging and activation of the integrated stress response in the mouse heart

    Ranea-Robles, Pablo, Pavlova, N. N., Bender, A., Pereyra, A. S., Ellis, J. M., Stauffer, B., Yu, C., Thompson, C. B., Argmann, C., Puchowicz, M. & Houten, S. M., 29 Dec 2022, In: Cardiovascular Research.

    Research output: Contribution to journalJournal articleResearchpeer-review

  2. Aberrant regulation of the GSK ‐3β/ NRF 2 axis unveils a novel therapy for adrenoleukodystrophy

    Ranea-Robles, Pablo, Launay, N., Ruiz, M., Calingasan, N. Y., Dumont, M., Naudí, A., Portero‐Otín, M., Pamplona, R., Ferrer, I., Beal, M. F., Fourcade, S. & Pujol, A., 11 Aug 2018, In: EMBO Molecular Medicine.

    Research output: Contribution to journalJournal articleResearchpeer-review

  3. Published

    Cross-species comparison of pregnancy-induced GDF15

    Klein, A. B., Ranea-Robles, Pablo, Nicolaisen, T. S., Gil, Cláudia, Johann, K., Prats Quesada, Júlia, Pistoljevic, N., Hviid, K. V. R., Olsen, L. F., Offersen, Simone Margaard, Helge, Jørn Wulff, Nielsen, Henriette Svarre, Bakker, J., Kleinert, Maximilian & Clemmensen, Christoffer, 2023, In: American Journal of Physiology - Endocrinology and Metabolism. 325, 4, p. E303-E309

    Research output: Contribution to journalJournal articleResearchpeer-review

  4. Dietary restriction in the long-chain acyl-CoA dehydrogenase knockout mouse

    Diekman, E. F., van Weeghel, M., Suárez-Fariñas, M., Argmann, C., Ranea-Robles, Pablo, Wanders, R. J. A., Visser, G., van der Made, I., Creemers, E. E. & Houten, S. M., Jun 2021, In: Molecular Genetics and Metabolism Reports. 27, p. 100749

    Research output: Contribution to journalJournal articleResearchpeer-review

  5. Published

    GLP-1-directed NMDA receptor antagonism for obesity treatment

    Petersen, J., Ludwig, M. Q., Juozaityte, V., Ranea-Robles, P., Svendsen, C., Hwang, E., Kristensen, A. W., Fadahunsi, N., Lund, J., Breum, A. W., Mathiesen, C. V., Sachs, L., Moreno-Justicia, R., Rohlfs, R., Ford, J. C., Douros, J. D., Finan, B., Portillo, B., Grose, K., Petersen, J. E. & 13 others, Trauelsen, Mette, Feuchtinger, A., DiMarchi, R. D., Schwartz, Thue W., Deshmukh, Atul Shahaji, Thomsen, Morten Bækgaard, Kohlmeier, Kristi Anne, Williams, K. W., Pers, Tune H, Frølund, Bente, Strømgaard, Kristian, Klein, A. B. & Clemmensen, Christoffer, 2024, In: Nature. 629, 8014, p. 1133–1141

    Research output: Contribution to journalJournal articleResearchpeer-review

  6. Metabolic interactions between peroxisomes and mitochondria with a special focus on acylcarnitine metabolism

    Houten, S. M., Wanders, R. J. A. & Ranea-Robles, Pablo, May 2020, In: B B A - Molecular Basis of Disease.

    Research output: Contribution to journalJournal articleResearchpeer-review

  7. Modulation of mitochondrial and inflammatory homeostasis through RIP140 is neuroprotective in an adrenoleukodystrophy mouse model

    Ranea-Robles, Pablo, Galino, J., Espinosa, L., Schlüter, A., Ruiz, M., Calingasan, N. Y., Villarroya, F., Naudí, A., Pamplona, R., Ferrer, I., Beal, M. F., Portero‐Otín, M., Fourcade, S. & Pujol, A., Feb 2022, In: Neuropathology and Applied Neurobiology.

    Research output: Contribution to journalJournal articleResearchpeer-review

  8. Published

    Murine deficiency of peroxisomal L-bifunctional protein (EHHADH) causes medium-chain 3-hydroxydicarboxylic aciduria and perturbs hepatic cholesterol homeostasis.

    Ranea-Robles, Pablo, Violante, S., Argmann, C., Dodatko, T., Bhattacharya, D., Chen, H., Yu, C., Friedman, S., Puchowicz, M. & Houten, S., Jun 2021, In: Cellular and molecular life sciences : CMLS.

    Research output: Contribution to journalJournal articleResearchpeer-review

  9. Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease

    Ruiz, M., Bégou, M., Launay, N., Ranea-Robles, Pablo, Bianchi, P., López-Erauskin, J., Morató, L., Guilera, C., Petit, B., Vaurs-Barriere, C., Guéret-Gonthier, C., Bonnet-Dupeyron, M., Fourcade, S., Auwerx, J., Boespflug-Tanguy, O. & Pujol, A., Sep 2018, In: Brain Pathology. 28, 5, p. 611-630 20 p.

    Research output: Contribution to journalJournal articleResearchpeer-review

  10. Peroxisomal L-bifunctional Protein Deficiency Causes Male-specific Kidney Hypertrophy and Proximal Tubular Injury in Mice

    Ranea-Robles, Pablo, Portman, K., Bender, A., Lee, K., He, J. C., Mulholland, D. J., Argmann, C. & Houten, S. M., 30 Sep 2021, In: Kidney360.

    Research output: Contribution to journalJournal articleResearchpeer-review

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