Pablo Ranea Robles

Pablo Ranea Robles

Postdoc

ORCID: 0000-0001-6478-3815

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  1. Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease

    Ruiz, M., Bégou, M., Launay, N., Ranea-Robles, Pablo, Bianchi, P., López-Erauskin, J., Morató, L., Guilera, C., Petit, B., Vaurs-Barriere, C., Guéret-Gonthier, C., Bonnet-Dupeyron, M., Fourcade, S., Auwerx, J., Boespflug-Tanguy, O. & Pujol, A., Sep 2018, In: Brain Pathology. 28, 5, p. 611-630 20 p.

    Research output: Contribution to journal › Journal article › Research › peer-review

  2. Slc22a5 haploinsufficiency does not aggravate the phenotype of the long‐chain acyl‐CoA dehydrogenase KO mouse

    Ranea-Robles, Pablo, Yu, C., Vlies, N., Vaz, F. M. & Houten, S. M., 23 May 2020, In: Journal of Inherited Metabolic Disease.

    Research output: Contribution to journal › Journal article › Research › peer-review

  3. Aberrant regulation of the GSK ‐3β/ NRF 2 axis unveils a novel therapy for adrenoleukodystrophy

    Ranea-Robles, Pablo, Launay, N., Ruiz, M., Calingasan, N. Y., Dumont, M., Naudí, A., Portero‐Otín, M., Pamplona, R., Ferrer, I., Beal, M. F., Fourcade, S. & Pujol, A., 11 Aug 2018, In: EMBO Molecular Medicine.

    Research output: Contribution to journal › Journal article › Research › peer-review

  4. Modulation of mitochondrial and inflammatory homeostasis through RIP140 is neuroprotective in an adrenoleukodystrophy mouse model

    Ranea-Robles, Pablo, Galino, J., Espinosa, L., Schlüter, A., Ruiz, M., Calingasan, N. Y., Villarroya, F., Naudí, A., Pamplona, R., Ferrer, I., Beal, M. F., Portero‐Otín, M., Fourcade, S. & Pujol, A., Feb 2022, In: Neuropathology and Applied Neurobiology.

    Research output: Contribution to journal › Journal article › Research › peer-review

  5. A mitochondrial long-chain fatty acid oxidation defect leads to transfer RNA uncharging and activation of the integrated stress response in the mouse heart

    Ranea-Robles, Pablo, Pavlova, N. N., Bender, A., Pereyra, A. S., Ellis, J. M., Stauffer, B., Yu, C., Thompson, C. B., Argmann, C., Puchowicz, M. & Houten, S. M., 29 Dec 2022, In: Cardiovascular Research.

    Research output: Contribution to journal › Journal article › Research › peer-review

  6. Published

    The physiology of experimental overfeeding in animals

    Ranea-Robles, Pablo, Lund, Jens & Clemmensen, Christoffer, 2022, In: Molecular Metabolism. 64, 15 p., 101573.

    Research output: Contribution to journal › Review › Research › peer-review

  7. The peroxisomal transporter ABCD3 plays a major role in hepatic dicarboxylic fatty acid metabolism and lipid homeostasis

    Ranea-Robles, Pablo, Chen, H., Stauffer, B., Yu, C., Bhattacharya, D., Friedman, S. L., Puchowicz, M. & Houten, S. M., 2021, In: Journal of Inherited Metabolic Disease. 44, 6, p. 1419-1433 15 p.

    Research output: Contribution to journal › Journal article › Research › peer-review

  8. Peroxisomal L-bifunctional Protein Deficiency Causes Male-specific Kidney Hypertrophy and Proximal Tubular Injury in Mice

    Ranea-Robles, Pablo, Portman, K., Bender, A., Lee, K., He, J. C., Mulholland, D. J., Argmann, C. & Houten, S. M., 30 Sep 2021, In: Kidney360.

    Research output: Contribution to journal › Journal article › Research › peer-review

  9. The peroxisomal transporter ABCD3 plays a major role in dicarboxylic fatty acid metabolism

    Ranea-Robles, Pablo, Chen, H., Stauffer, B., Yu, C., Bhattacharya, D., Friedman, S. L., Puchowicz, M. & Houten, S. M., 2021, bioRxiv, 39 p.

    Research output: Working paper › Preprint › Research

  10. Published

    The biochemistry and physiology of long-chain dicarboxylic acid metabolism

    Ranea-Robles, Pablo & Houten, S. M., 2023, In: Biochemical Journal. 480, 9, p. 607-627 21 p.

    Research output: Contribution to journal › Review › Research › peer-review

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